Wednesday 20 February 2008

Mondini deformity

Middle and apical turns are fused, basal turn is present

a/w deformities of vestibule, SCC, endolymphatic duct, endolymphatic sac

Present with low frequency hearing loss

Cochlear implants are done. May be associated with defect of modiolus. Placing electrode can empty endolymph, hence it is important to assess modilous. Modilolus can be measured on MR.

May suffer with recurrent meningitis, due to spontaneous fistula between middle ear and subarachnoid space